Paediatric Pulmonology and Allergology

2003 October, Vol. VI, No. 2 (pp.2290-2296)

Congenital lobar emphysema

Stanislovas Maknavicius, Gintas Posiunas, Zydrune Prapuoleniene

In the pe­riod from 1981 to 2002 we are in­ves­ti­ga­ted 19 chil­dren with con­ge­ni­tal lo­bar emp­hy­se­ma – 13 bo­ys and 6 girls. Pa­tients age: 3 new­borns (1 day – 1; 4 da­ys – 1 and 5 da­ys – 1), 1 month – 2 pa­tients, 2-3 month – 3 pa­tients, 4-6 month – 5 pa­tients, 1-2 year – 2 pa­tients, ol­der – 3 pa­tients. 11 pa­tents had pat­ho­lo­gi­cal fin­dings in the right lung and 8 pa­tents  - in the left lung. Most of­ten emp­hy­se­ma was lo­ca­li­zed in the mid­dle lo­be of the right lung (8 ca­ses) and in up­per lo­be of the left lung (7 ca­ses). In 10 ca­ses it was found con­co­mi­tant pat­ho­lo­gy: con­ge­ni­tal he­art di­se­a­se, neu­ro­mus­cu­lar di­se­a­se, bron­chop­leu­ral fis­tu­la, etc. Res­pi­ra­to­ry di­stress syn­dro­me was the most fre­qu­ent pro­blem of all our pa­tients. We found on­ly 3 pa­tients wit­hout cli­ni­cal signs of res­pi­ra­to­ry in­suf­fi­cien­cy. Lo­bec­to­my we­re per­for­med in 18 pa­tients, 3 of them died af­ter sur­gi­cal tre­at­ment.

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